Hypertrophic Cardiomyopathy

Management

  1. Family screening and genetic counseling for all first degree relatives
  2. Avoid volume depletion
  3. Beta-blockers are first line (they do NOT reduce sudden cardiac death)
  4. Consider procedural interventions (septal myomectomy, ETOH ablation)
  5. consider ICD for:
    1. Sustained VT or prior cardiac arrest (Class I)
    2. FMHx of sudden death, thick LV wall > 30 mm, unexplained syncope (Class IIa)